Paraganglioma of the organ of Zuokerkandl is a rare tumor that arises from the paraaortic paragnglia around the origin of the inferior mesenteric artery.
Paragangliomas are usually recognized by the effects of overproduction of catecholamines. The diagnosis of paraganglioma is confirmed by clinical symptoms, biochemistry and radiologic localization. Because about 10% incidence of malignancy and no
reliable histopathologic features distinguishing malignnt paraganglioma, complete surgical resection and prologed follow up are indicated. We present a case of paraganglioma arising from the organ of Zuckerkandl..
The patient was a 20-year-old woman with the complaints of headache, abdominal pain and vomiting. Paraganglioma was suspected by elevated level of plasma catecholamines and their metabolites, and ws confirmed by computed tomographic scan and
aortic
angiography.
The mass, measuring 4×3, 5×3cm and weighing 32gm, was completely resected by means of transperitoneal approach and proved to be a benign paraganglioma pathologically. Postoperatively, plasma catecholamine and blood pressure were normalized, and
symptoms were improved.
|